Term
|
Definition
| Amoxicillin + Clavulanic acid, Dicloxacillin, 1st/2nd cephalosporin |
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|
Term
|
Definition
| Trimethoprim/Sulfamethoxazole, Doxycycline, Minocycline, Clindamycin, Linezolid |
|
|
Term
|
Definition
| Trimethoprim/Sulfamethoxazole or minocycline |
|
|
Term
|
Definition
| Ciprofloxacin or Levofloxacin |
|
|
Term
| Pathogens causing early infections |
|
Definition
| SA, H-Flu, P. Aeruginosa, |
|
|
Term
| Rare bacteria common in CF |
|
Definition
| Burkholderia cepacia and Stenotrophomonas maltophilia |
|
|
Term
|
Definition
| uses pilocarpine iontophoresis to diagnose CF; Cl conc. > 60 mEq/L |
|
|
Term
| Dornase Alfa (adult and pediatric dose) |
|
Definition
| 2.5 mg nebulized 1-2 x daily |
|
|
Term
| Ibuprofen (adult and pediatric dose) |
|
Definition
| 20-30 mg/kg/dose twice daily |
|
|
Term
| Azithromycin (pediatric dose) |
|
Definition
| 25-39 kg give 250 mg on Mon, Wed, Fri |
|
|
Term
| Azithromycin (adult dose) |
|
Definition
| 40 kg or more give 500 mg on Mon, Wed, Fri |
|
|
Term
|
Definition
| inhibits lipoxygenase pathway, reducing neutrophil migration and function as well as release of lysosomal enzymes |
|
|
Term
|
Definition
| cleaves DNA released during neutrophil degradation that contributes to the high viscosity of CF sputum |
|
|
Term
|
Definition
| maybe by interference with pseudomonas alginate biofilm production, bactericidal activity during stationary Pseudomonas growth, neutrophil inhibition, interlukin-8 reduction, and reduction in sputum viscosity |
|
|
Term
| Pancreatic Enzyme starting dose (adult) |
|
Definition
| 500 - 1000 units/kg/meal of lipase component (1/2 for snacks) |
|
|
Term
| Pancreatic Enzyme starting dose (infant) |
|
Definition
| 1500 - 2500 units of lipase per 120 mL of formula or breast milk |
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|