Term
| tx for posterior uveitis vs. anterior uveitis in sarcoidosis |
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Definition
| posterior: systemic steroids; anterior: topical steroids |
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Term
| what defines each stage in sarcoidosis? |
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Definition
| 1. hilar adenopathy, no lung involvement; 2. hilar adenopathy+lung involvement; 3. no adenopathy, lung involvement; 4. fibrosis |
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Term
| immune profile in a pt with sarcoidosis |
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Definition
| Th1>Th2, anergy, oligoclonal CD4 T cells, polyclonal hypergammaglobulinemia |
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Term
| organs involved in sarcoidosis |
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Definition
| lung, skin (nodules, plaques, scales), eyes (iritis, uveitis), spleen (-megaly), bone marrow |
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Term
| noncaseating granulomas, TB culture negative, no nephropathy, pANCA-, cANCA-, no eosinophilia, |
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Definition
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Term
| child presents with dry airways, dry and persistent cough, Sjogren's; dx? |
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Definition
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Term
| pANCA+, eosinophilia; dx? |
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Definition
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Term
| cANCA+, saddle-nose deformity, glomerulonephritis, pulmonary granulomas; dx? |
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Definition
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Term
| HRCT: nodules next to thin-walled cysts; dx? |
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Definition
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Term
| stellate nodules, spares CVA; dx? |
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Definition
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Term
| ILD more common in smokers |
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Definition
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Term
| defect in sphingomyelinases |
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Definition
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Term
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Definition
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Term
| granulomatous colitis, ILD |
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Definition
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Term
| DAH, glomerulonephritis; dx? |
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Definition
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Term
| female with pneumothorax; HRCT: thin-walled cysts surrounded by normal lung; dx? |
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Definition
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Term
| elevated LDH, polycythemia, hypergammaglobulinemia |
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Definition
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Term
| leukemic pt with "bat-wing" CXR; dx? |
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Definition
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Term
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Definition
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Term
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Definition
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Term
| pregnant female with UTI presents with hypersensitivity pneumonitis; what drug is she taking? |
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Definition
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Term
| pt with hx of Hodgkin's lymphoma presents with interstitial lung disease; what drug is responsible? |
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Definition
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Term
| pt with hx of atrial fibrillations is worked up for ILD. HRCT shows an image as if contrast was given but it was not; what drug is responsible? |
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Definition
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Term
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Definition
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Term
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Definition
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Term
| pleuritis +/- effusion, anti-dsDNA+; dx? |
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Definition
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Term
| RA, necrobiotic nodules, pneumoconiosis; dx? |
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Definition
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Term
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Definition
| male coal miner with pleuritis +/- effusion, necrobiotic nodules +/- cavitations, Caplan's syndrome |
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Term
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Definition
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Term
| HRCT: bilateral, subpleural ground glass opacities without honeycombing; dx? |
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Definition
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Term
| HRCT: bilateral, patchy ground glass or consolidation. Biopsy: hyaline membranes; dx? |
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Definition
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Term
| clinical presentation of AIP |
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Definition
| 2 weeks of prodrome illness then dry cough, fever, dyspnea, then hypoxemia and respiratory failure |
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Term
| macrophages in alveolar space with little interstitial fibrosis |
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Definition
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Term
| what would you find on a HRCT in a pt with IPF? |
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Definition
| patchy, basilar subpleural reticular opacities, traction bronchiectasis, honeycombing |
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Term
| what would you find on a lung biopsy in a pt with IPF? |
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Definition
| fibrotic foci, heterogenous at subpleural parenchyma |
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Term
| where can BAL be used to diagnose and confirm? (4) |
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Definition
| sarcoidosis, hypersensitivity pneumonitis, PAP, DAH, cancer |
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Term
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Definition
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Term
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Definition
| hypersensitivity pneumonitis |
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Term
| eosinophilic pneumonitis, hypersensitivity pneumonitis are [acute/subacute/chronic/episodic] |
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Definition
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Term
| sarcoidosis, drug, CTD, COP are [acute/subacute/chronic/episodic] |
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Definition
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Term
| sarcoidosis, CTD, IPF, PLCH, pneumoconiosis is [acute/subacute/chronic/episodic] |
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Definition
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Term
| characteristics of impaired repair |
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Definition
| fibrin, fibroblasts, myofibroblasts, type II cells replace type I cells, new blood vessels, more ECM, reduced surface area |
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