Term
| Embrylogically when do most congenital heart diseases develop |
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Definition
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Term
| What heart defect is associated with maternal rubella infections |
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Definition
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Term
| What is the most common congenital haert defect? |
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Definition
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Term
| What is the most common cyanotic congenital heart disease |
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Definition
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Term
| When would you want to keep a patent ductus open and how would you do it? |
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Definition
Transposition of the Great Vessels
PGE2 Administration |
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Term
| What congenital Heart Defect is associated with Marfan's syndrome |
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Definition
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Term
| What congenital heart disease is associate with Down's Syndrome |
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Definition
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Term
| What congenital heart disease is associated with Turner's syndrome |
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Definition
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Term
| What is Cyanosis Tardive and When would you see it? |
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Definition
Shunt reversal making the patient cyanotic
Occurs when Pulmonary HPTN causes Right heart pressure to equal left heart pressure
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Term
| What would be some possible cues of a long standing right-left shunt |
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Definition
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Term
| What Left right shunt will lead to pulmonary hypertension and which will not |
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Definition
Will: VSD, PDA, ASVD
Will not: ASD |
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Term
| What is the effect of increased pressure on pulmonary arteries |
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Definition
| Medial Hypertrophy and vasoconstriction-> Obtructive Intimal Lesions-> Increase Pulmonary resistance |
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Term
| Location of the most common ASD |
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Definition
| Incompitance of Fossa Oval |
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Term
| What valvular disorder is a secundum ASD associated with? |
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Definition
| Cleft Anterior Mitral Valve |
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Term
| What is a Sinus Venosis ASD |
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Definition
| Usually a SVC-Rt. Pulmonary Vein connection |
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Term
| What is the prognosis for a ASD |
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Definition
Only 10% develop Pulmonary HPTN
Surgery can prevent complications |
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Term
| What characteristics of a VSD have a better prognosis |
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Definition
| Small VSD in the Muscular Septum |
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Term
| What are the mechanisms to close a patent ductus |
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Definition
Endometacin
Catheter implant
Surgery |
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Term
| What the characteristics of Tetrology of Fallot |
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Definition
Over-riding aorta
Pulmonary Stenosis
VSD
RV Hypertropy |
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Term
| What determines the severity of tetrology of fallot |
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Definition
| degree of pulmonary stenosis |
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Term
| What congenital heart disease will produce a boot shaped heart |
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Definition
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Term
| What congenital heart disease is associated with digeorge syndrome |
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Definition
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Term
| When is Transposition of the great vessels at least initially compatible with life |
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Definition
VSD
Patent Ductus
Patent Foramen Ovale |
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Term
| What are some diagnostic clue for coarctation of the aorta |
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Definition
Bounding Upper Pulses w/ Faint Lower Pulses
Rib Notching on CXR from Collaterals
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Term
| What are common abnormalities associated with a completely Atretic pulmonary valve |
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Definition
Hypoplastic R. Ventricle
ASD |
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Term
| What is the morphology of the heart with a completely atretic Aortic valve |
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Definition
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Term
| What are the sites of Aortic Atresia |
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Definition
Subaortic
Valvular
Supravalvular |
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Term
What percetnt of live births have a congenital heart defect
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Definition
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