| Term 
 | Definition 
 
        | the ubiquitin proteosome requires what for activation? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what provides the correct pH for gastric enzymes to be active |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | pancreatic enzymes are released as zymogens. what hormone is responsible for this release |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | at the C-terminal this lyses Alanine, Leucine, Isoleucine, Valine |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | at the C-terminal this lyses Arginine or Lysine |  | 
        |  | 
        
        | Term 
 
        | Alanine, Glycine, and Serine |  | Definition 
 
        | Elastase, which is activated by trypsin, lyses what three AA on the C-side? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | Amino acids require pyridoxal phophate which is derived from? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | Alanine and alpha-ketoglutarate are the reactants and pyruvate and glutamate are the products of this enzyme |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | OAA and Glutamate are the reactants and Asparate and alpha ketoglutarae are the products of this enzyme |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | Leucine, Lycine, and Tryptophan are the major? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | AR disorder where cystine cant be reabsorbed and leadds to stones of cystine in the urinary tract |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | all of the amino acids except these two participate in transamination |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | NAD+ and NADP can be used as coenzymes for this enzyme |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what is the allosteric inhibitor of glutamate dehydrogenase? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what is the allosteric activator of glutamate dehydrogenase? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what is the precursor for ammonium and asparate nitrogen? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what allosterically activates carbomyl synthestase I? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | what is the activator of NAG |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | how many molecules of ATP are consumed in the formation of UREA |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | reduces the number of intestinal bacteria responsible for NH3 production |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | how many high energy phosphates are consumed in the synthesis of each mole of urea? |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | carbamoyl phosphate synthestase I deficiency is treated with? |  | 
        |  | 
        
        | Term 
 
        | carbomyl phophate synthetase I |  | Definition 
 
        | a deficiency in this enzyme, leads to the inability for nitrogenous waste to be metabolized in the urea cycle |  | 
        |  | 
        
        | Term 
 
        | Orthinine Transcarbomylase |  | Definition 
 
        | a deficiency in this enzyme leads to a inability for nitrogenous waste to be metabolized and is associated with X-linked inheritance |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | a deficiency in this enzyme leads to a elevated serum citrulline count associated with hypotonia, ataxia, and behavioral changes |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | a deficiency in this enzyme leads to hyperammonemia and has huge effects on the CNS |  | 
        |  | 
        
        | Term 
 | Definition 
 
        | if there is a deficiency in this enzyme there will be no hyperammonemia and there will be restoration of the pathway |  | 
        |  |